Mermaid baby or Sirenomelia: A rare congenital anomaly

Nital Kumar Sarker1, Probir Kumar Sarkar2, Farid Ahmed3, Jotsna Ara Begum4, Mohammed Hanif5

Introduction
Mermaid Syndrome, alternatively known as
Sirenomelia is an extreme example of the caudal
regression syndrome.1 It is a very rare congenital
deformity in which the legs are fused together,
giving them the appearance of a mermaid’s tail. This
condition is found in approximately one out of every
100,000 live births (about as rare as conjoined twins)
and is usually fatal within a day or two of birth
because of complications associated with renal
agenesis or abnormal kidney and urinary bladder
development and function.2 Other associated
malformations include absent external genitalia,
imperforated anus, lumbosacral, vertebral and pelvic
abnormalities and CNS malformation.3,4 Maternal
diabetes has been associated with caudal regression
syndrome and sirenomelia where the relative risk
is 1:200 - 250.5 VACTERL-H is an expanded form of
the VACTERL association that concludes that this
diagnosis is a less severe form of sirenomelia.6 Here
we present a case of Mermaid Syndrome in a 6 hours old newborn.

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